A Potentially Life-threatening Condition
PAH gets worse over time and can be life threatening, especially for people with scleroderma.1
Who Is at Risk for PAH?
If you have scleroderma, you are at risk for PAH.4
African Americans with scleroderma may develop PAH more frequently than the overall population of people with scleroderma.6
A study from 2003 showed the rate of PAH was higher in 130 African Americans with scleroderma (48%) than in the overall population of 709 people in the scleroderma center (39%).
Other Risk Factors for PAH
Additional factors that can increase your risk include4,7:
Older age at the time of your scleroderma diagnosis
If you have had scleroderma for a long time
A condition in which small blood vessels in the hands and toes spasm in the cold
Spider veins on your skin but may develop anywhere within the body
Painful pale, white, or blue fingers
A type of scleroderma in which skin hardening and tightening occurs only on the fingers, hands, forearms, and face
Presence of certain antibodies
Results in the low range on certain pulmonary function tests
What Is PAH?
PAH is a disease of high blood pressure in the lungs that can be more common in people with scleroderma.4,8Find out more